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Micropenis

In neonates and infants, the stretched penile length is at least 2cm in 97% of boys.

Micropenis describes a shorter penis than this, that is otherwise of normal form. Penis needs to be stretched out, and suprapubic fat pad pushed in.

Causes are hypogonadotrophic (Kallman’s syndrome, Laurence-Moon-Biedel-Bart, Prader-Willi) or hypogonadism (anorchia or testicular dysgenesis, Trisomy 21, Noonans, Klinefelter). May be part of more complex syndrome.

Differential is intersex, “buried penis” due to suprapubic fat pad (usually obese), chordee.

Neat trick is to modify a 10ml syringe by cutting off needle end and inserting plunger into cut end. Gives you scale and stretches penis!

[https://dx.doi.org/10.4274%2FJcrpe.1135]

Contact dermatitis

Type 4 delayed hypersensitivity seen to a range of things including:

  • Nickel (for example in jewellery, belt buckles, fastenings)
  • Limonene, found in many cleaning products and cosmetics
  • Sodium lauryl sulfate, found in cleaning products and cosmetics
  • Lanolin and other wool products

Mechanism is complicated as metals are clearly not proteins so not identified by HLA class 2 as happens in type 1 allergy. Presumably happens through toll like receptors.

Testing is by patch testing, done by dermatology.

Delayed puberty

Note puberty lines on RCPCH growth charts, for starting puberty (girls 8), delayed beginning (girls 13, boys 14) and completing (girls 16, boys 17).  Delayed completion (especially menses) also needs investigation.  Also a shaded triangle for short boys and girls during this time, to remind that probably ok if puberty not yet started, but potentially a problem if nearly completing.

In girls, rule out Turner’s syndrome.

Otherwise look for evidence of dysmorphism, that might suggest another chromosomal or genetic issue, and evidence for broader pituitary issue (midline facial defects, visual defects, poor growth, child looks younger than their age).

If not central, then must be gonadal issue – check testes, do USS scan to look at ovaries.

Blood tests then to assess pituitary hormones, particularly FSH/LH, plus oestradiol and testosterone.

In girls with amenorrhoea but normal pubertal progression, haematocolpos due to imperforate hymen presents with abdominal pain, urinary retention.

Scarlet Fever

Has Victorian connotations as fatal epidemics of Scarlet fever swept through slums in the pre-antibiotic era.

Group A streptococcus pyogenes is still carried in up to 20% of young children’s throats. Disease peaks in winter and spring (cool conditions, and more time indoors?). Spread easily through saliva.

Scarlet fever (scarlatina is usually used for mild cases) is when an exotoxin is produced, that causes fever and rash. Characteristic features are:

  • Strawberry tongue – progresses from white coated, to red, beefy tongue as coating lifts.
  • Perioral pallor
  • Fiery, widespread rash – rough “sandpaper” feel characteristic
  • Pastia’s lines – lines of petechiae in creases esp wrists, elbows
  • Palatal petechiae (“Forchheimer spots”) – not specific, also measles. 
  • As rash fades, desquamation can occur, particularly on fingers/toes. Should only happen once in lifetime, as antibodies form to toxin!?

No longer notifiable in Scotland, cf England/Wales.

Complications can still be severe of course, as with any group A strep disease:

Benefit of antibiotic treatment just ½ day symptoms! But without treatment would need to exclude from nursery/school for 14 days!!! Else after 24hrs antibiotics.

No resistance to penicillin and low MIC so preferred. 10 day course of whichever antibiotic recommended (for clearance from throat, as opposed to clinical improvement), with exception of azithromycin (5 days).

Other antibiotics eg clindamycin may be chosen however if invasive disease.

Allergy and Transition

Although transition is usually meant to describe a process of passing on medical care to an adult service for a chronic condition, with allergy things are a bit different. Firstly, the diagnosis is often made at a very young age and the child may have lived with it for many years before the age where transition processes generally kick in (around 11-13yrs, often coinciding with move to high school), so they may already be very aware of their condition.

Secondly, there is often no need for adult allergy service input, and in some areas eg Eastern Scotland there is no adult allergy service anyway.

The challenge is that young people want independence from their parents, self – determination, at the same time they want to fit in with their peers. It is the developmental task of adolescence to have new experiences (even if they are not as bullet proof as they might imagine), including sexual/intimate relationships. It is normal, indeed appropriate, for them to challenge authority/norms, take risks, experiment, demand rights.

When it comes to allergies, bad eczema may already have affected self-image, self-esteem, caused social isolation.  Asthma may have reduced participation in sports, and has its own negative stereotypes.

It’s sometimes productive to go back in the history, especially where there is a history of anaphylaxis – how much is chronic parental anxiety, how much terror of further reaction. 

Non-judgmental approach important.  Particularly important for a young people to be treated as an individual.  When it comes to risks and safety, key in allergy, it’s all about balance – fear of reaction vs being “normal”.  Requires negotiation.

“I have found the best way to give advice to children is to find out what they want and then advise them to do it.” [Harry Truman]  “When I was a boy of 14, my father was so ignorant I could hardly stand to have the old man around. But when I got to be 21, I was astonished at how much the old man had learned in seven years”. [Mark Twain]

EAACI has 2020 guidance, combined allergy and asthma, by Graham Roberts in Southampton. Key points are:

  • Do you use a structured multidisciplinary transition programme for allergy?
  • Do you use a checklist of skills and knowledge to assess readiness for transition?
  • Do you communicate with your young persons via text or other mobile technology?
  • Do you discuss exams and impact of allergic rhinitis?
  • Have you had any specific teaching or training in transitional care (generic and/or allergy specific)?
  • Do you recommend any specific websites or apps for allergy advice/support?
  • Do you focus consultation on areas where young person says they are not confident?
  • Do you provide (“formulate”)  a personal allergy plan?
  • Do you offer information about any peer-led interventions?
  • Do you discuss exams and impact of allergic rhinitis?
  • Do you recommend any specific websites or apps for allergy advice/support?
  • Do you focus consultation on areas where young person says they are not confident?
  • Do you provide (“formulate”)  a personal allergy plan?
  • Do you identify psychosocial issues, using a tool such as YouthCHAT (online, 8 mins) – includes physical inactivity, eating disorder, problems at home, sexual health etc.
  • Do your friends understand you have an allergy and how to manage an emergency?
  • Do your teachers understand you have an allergy?
  • Do you signpost to high quality online resources?  Do you discuss the role of social media [ie how moderation is desirable, to keep chat positive]
  • [other stuff more relevant probably to asthma]

CYANS is similar, suggesting bite sized topics including:

  1. Do you confirm that they know their diagnosis accurately, and are not avoiding any foods unnecessarily?
  2. Do you discuss specific foods/cuisines that they need to be careful with?
  3. Do you discuss the potential risk from foods labelled “May contain…” or with similar precautionary labels?
  4. Do you discuss experience of food shopping and cooking?
  5. Do you check how confident they feel explaining their allergy to others?
  6. Do you discuss the potential for alcohol to increase the risk of anaphylaxis?
  7. Do you discuss the potential risk from kissing?
  8. Do you present a scenario of an unexpected reaction, to check their understanding of anaphylaxis symptoms and appropriate self management?
  9. Do you see them alone (with parental agreement)?

Tissue viability

Typically a combination of moisture damage and pressure. Prevention obviously essential. Wash, clean and dry first.

Treat any infection.

For excoriation –

  • Medi Derma S barrier cream
  • Medi Derma S film for more severe – comes as pump spray or topical applicator

Dravet syndrome

Previously Severe myoclonic epilepsy of infancy. Charlotte Dravet described in 70s. Characterised by:

  • Refractory epilepsy
  • Onset in infancy
  • Associated neurodevelopmental problems

Due to defect in SCN1A gene on chromosome 2q24 (a sodium channel), usually de novo. Many mutations, don’t predict severity, unfortunately.

Accounts for about 7% of epilepsy presenting in first 3 years of life.

Onset around 5-8 months, often with febrile illness so can look like typical febrile convulsion. But often prolonged. Neurodevelopmental problems come later…

Later though, multiple seizure types. Hypotonia, ataxia, spasticity all seen. Dysautomnia can be a feature. ADHD and autistic traits common later.

EEG can be normal, or vary over time, with multifocal or generalised changes, photosensitivity too.

Racism in Medicine

Infant mortality for black babies in US double that of white babies.

Newborn mortality in Florida for black babies under care of black doctors 58% lower than those under white doctors. No difference for white babies. Still not as good as white mortality though.

Confidence as a doctor

As a doctor, you want to feel confident in your abilities and your diagnosis, you certainly don’t want to question yourself constantly. Equally, your patients want to feel confident that you know what you are talking about, and will probably get better more quickly if they do (placebo effect).

Most people can smell bullsh*t from a mile off if you try to say something you don’t actually think or believe. Typically, your words (vague) and body language (evasive) will give you away.

At the same time, the over confident doctor is dangerous. Arrogance is also very unattractive. So there is a balance.

What do we mean by confident?

Confidence is a sense of belief in one’s own abilities. But of course you can have a strong belief in your own ability when you have no talent at all. So the kind of confidence we want to have is probably the sense of certainty that you can do something reasonably well, even that you can then do it without really needing to think too much about it at all.

It isn’t a character trait! And of course there isn’t such a thing as a “confident person”, because it depends on the skill being considered. Great athletes can be terrible public speakers, for example.

Ironically, genuine humility has a role to play in establishing or reestablishing your sense of self-assurance.  High self esteem spills over into narcissism. Overly positive (or indiscriminate, at any rate) self belief may contribute to low motivation and a decrease in goal-directed behavior.

Self worth or self efficacy? The latter is forward looking, the other is perhaps more static, on the basis of internalised judgements. Self worth can be linked to social acceptance/rejection in Leary’s Sociometer theory (based in evolutionary psychology), and certainly exclusion on the basis of personal characteristics lowers self esteem. 

How do get more confident?

It’s cultivated by early childhood experiences of course. How were you encouraged to think about your own efforts and abilities? But no reason you can’t gain in confidence, or at least make your confidence commensurate with your competency. Some people may have more baggage to deal with, of course.

So first step must be to gain competency – which means understanding the basics, practising the skills, and recognizing when things fall outside what you have seen so far. Repetition is key, clearly.

Secondly – if you feel you are straying outside your comfort zone, is there any way to get more information? Do you have notes you can check? Do you know which are the best resources? Do you have a person you can ask safely?

Thirdly – can you see what factors are hindering you from performing at your best? Tiredness? Distraction?

You have to let children fail sometimes, if they are to learn to handle disappointment. 

Is it actually about courage, not confidence? Fear exists for a reason. Courage is the noble trait of facing up to fear and deciding when the signpost can be discarded. Adrenaline can be enjoyed at lower levels. Mindfulness, exercise help. 

People tend to grossly underestimate the willingness of others to help. But helping others in turn also emphasises the skills you do have and your status in the social hierarchy.  

[https://positivepsychology.com/self-confidence]

The story you tell yourself

Of course you are not perfect. You will make mistakes. You will forget something. You cannot know everything. But is there anyone other than yourself who expects otherwise?

So rather than concentrating on the negatives (which is probably natural, given that in the evolutionary survival game, you really don’t want to end up wounded, poisoned, lost or dead as often as you get lucky), can you tell yourself that you are ready for this, that you are trained for this, you have worked for this, you work reasonably well in almost all conditions?

That mistakes do not cancel out everything you get right the rest of the time?

Although there is a time to be self critical, there are definitely just as many times if not more to be self friendly, and this can be hard for us if never modelled.

You need to practice positive self affirmations, if you want them to count when under stress. Confidence is like a bank balance that needs constant deposits. List the things you have done well in the past. Spend time each day reflecting on what went well. Spend time looking ahead and envisioning where you want to be. This should be the movie playing in your head.

The “shooter’s mentality” – any missed shot is a temporary slip, and just means the next shot will be successful. Any successful shot confirms that you are on a roll of consistent success.

And how do you think of other people’s success? Do you always equate confidence with arrogance, laziness, complacency?

Stand up straight with your shoulders back

Rule 1 of Jordan B Peterson’s 12 Rules for living.

“Standing up straight with your shoulders back is not something that is only physical, because you’re not only a body. Standing up means voluntarily accepting the burden of Being. You see the gold the dragon hoards, instead of shrinking in terror from the Dragon. It means deciding to transform the chaos of potential into the realities of habitable order. It means willingly undertaking the sacrifices necessary to generate a productive and meaningful reality.

“People, including yourself, will start to assume that you are competent (or at least they will not immediately conclude the reverse). Strengthened and emboldened, you may be able to stand, even during the illness of a loved one, even during the death of a parent, and allow others to find strength alongside you when they would otherwise be overwhelmed by despair.

“Then you may be able to accept the terrible burden of the world, and find joy. Look to the victorious lobster.”

See also the benefits of the Superman pose.

The cherry on top

Put in the work – the studying, the practice, the questioning, the reflection.

Then decide to tell yourself – “I’ve done the work. I know what I need to know. I’m going to deliver now. I am enough for this time and this place.”

Post operative ENT complications

Post adenoidectomy

Trickling blood behind uvula or hanging clot are reasons for re-exploration.

Post tonsillectomy

Secondary haemorrhage typically at 5-7 days.  Beware constant swallowing! White slough normal. Yellow (with pain) might mean infection so Corsodyl or peroxide gargles, 3-6x daily, possibly antibiotics.

History of bleeding but clear fossae – assess general condition and exclude bleeding disorder (family history), safety net.

If small clot, observe to see if enlarging. Every 15 mins or more if still spitting/swallowing. IV access and fast. Sit up.

Active bleeding needs anaesthetist for airway management, crossmatch too. Tonsil tray – adrenaline solution soaked swab applied to bleeding spot with Magill’s forceps until reaches theatre. Ice packs for back of neck. Post exploration NG tube to keep stomach empty.

Tranexamic acid, DDAVP? Eg vWD