=Asymmetric overgrowth of one limb, or one side of the body, or just one side of the face.
Can be associated asymmetric overgrowth of internal organs.
Essentially a cosmetic problem. But increased risk of tumours, including Wilm’s tumour, adrenal cell carcinoma, hepatoblastoma and small bowel sarcoma.
Risk of tumour development in isolated hemihyperplasia is about 1 in 20 or approximately 5%. Given that oldest reported case was 6yrs and shortest interval between tumour presentation and ultrasound was 5 months, suggested hat till age of 6 years these children should have abdominal ultrasound scans at three monthly intervals.